Complete Information on Beckwith-Wiedemann syndrome
Beckwith-Wiedemann Syndrome (BWS) is a congenital overgrowth syndrome, which can affect all systems of the body. It is associated with an elevated risk of embryonic tumor formation.
There is a 20% mortality rate for newborns with BWS. Macroglossia (large tongue), and macrosomia. Organomegaly, adrenocortical cytomegaly, hemihypertrophy, and neonatal hypoglycemia may also been seen. Macroglossia occurs in approximately 80% of cases and often results in ‘floppy’ airways. Which may require treatment with a tracheotomy. The cause of Beckwith-Wiedemann syndrome is genetic.
Complete Information on Adrenocortical carcinoma with Treatment and Prevention
Although adrenocortical carcinoma is rare in adults, it is even more uncommon in children.
Adrenocortical carcinoma is a rare malignancy with a poor prognosis. Adrenocortical carcinoma has no racial predilection. Also called adrenocortical cancer and cancer of the adrenal cortex. Adrenal carcinomas arise from the adrenal cortex and are bilateral in up to 10% of patients. The cause is unknown. About 2 people per million develop this type of tumor. Adrenocortical carcinoma has a bimodal occurrence, with the first peak in the first decade of life and the second peak in the fourth to fifth decades of life. Risk factors for adrenocortical carcinoma include having the following hereditary diseases: Li-Fraumeni syndrome, Beckwith-Wiedemann syndrome, Carney complex.
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